Multifocal inflammatory myofibroblastic tumor in the abdomen
نویسندگان
چکیده
A 17 year old so far healthy young man presented with upper abdominal pain. Imaging with sonography, MRT and PET-CT demonstrated three solid mass in the duodenal mesentery, pancreatic corpus and tail and on the upper pole of the left kidney. Open biopsy of the mesenterial mass revealed an inflammatory myofibroblastic tumor which was ALK-1 negative. Chemotherapy with vincristine, actinomycin D and cyclophosphamide was initiated and the imaging control after four cycles exhibited morphological and functional regression at all three mass locations. Surgery in curative intention was now performed and the nodules in the mesentery and the kidney were totally resected. The pancreas looked macroscopically normal and only biopsies were taken. Histology showed regressive fibrosis at all sites and no malignancy. The young man has now been well for now 50 months and follow-up imaging showed no sign of recurrence so far.
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